Congenital Differences-Distruption of the Radial/Ulnar Axis: Congenital Longitudinal Deficiencies

Distruption of the Radial/Ulnar Axis: Congenital Longitudinal Deficiencies

Pdf Summary

The article discusses the disruption of the radial/ulnar axis in congenital longitudinal deficiencies. Radial longitudinal deficiency (RLD) is often associated with abnormalities in other organ systems and requires a comprehensive medical evaluation. Ulnar longitudinal deficiency (ULD) tends to be associated only with musculoskeletal abnormalities. Central deficiency is a failure of hand plate formation and differentiation. In all of these conditions, there is a high incidence of thumb abnormalities, which often guide treatment. Surgery for RLD is controversial, with some advocating for centralization procedures and others favoring soft tissue procedures. Ulnar lengthening and ulnocarpal arthrodesis can also be considered. Treatment for ULD focuses on the function of the hand, with syndactyly releases, first webspace deepening, and thumb metacarpal rotational osteotomy being common procedures. Central deficiency is classified based on the first webspace, and surgical intervention may be necessary for cleft closure and associated anomalies. Psychological support is important for families and children coping with these conditions.

Keywords

radial longitudinal deficiency

ulnar longitudinal deficiency

congenital longitudinal deficiencies

thumb abnormalities

surgery for RLD

ulnar lengthening

ulnocarpal arthrodesis

treatment for ULD

central deficiency classification

psychological support